Rectal Carcinoma with a Large Amount of Mucin Production
in Childhood - Report of a Case
T. Todani, Y. Watanabe
Z Kinderchir 36: 73-75, 1982
A 10-year-old boy with rectal carcinoma underwent an abdominoperineal
resection with postoperative radiotherapy and chemotherapy. The tumor showed
a moderately differentiated adenocarcinoma with a large amount of mucin
production. Five years later, obstructive hydronephrosis due to postoperative
radiotherapy developed and uretero-ileo-cystoneostomy was performed after
transient bilateral nephrostomies. He is now I 7 years of age, 7 years after
the initial operation, and doing well with nearly normal renal function.
Colorectal carcinoma in childhood is very rare and has a poor prognosis,
which seems due to the high incidence of mucinous adenocarcinoma and delay
in early diagnosis. Besides polyp carcinoma with low grade malignancy, an
aggressive abdominoperineal resection with sigmoid colostomy is the treatment
of choice as in adults. Postoperative radiotherapy under a total of 3000
rads is also recommended for a better chance of cure. The effectiveness
of pre- and postoperative chemotherapy is still doubtful.
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