Congenital bile duct cysts: classification, operative procedures, and review of 37 cases including cancer arising from choledochal cyst

Takuji Todani, Yasuhiro Watanabe, Mitsuo Narusue, Katsusuke Tabuchi, Kunio Okajima

Am J Surg 134: 263-269, 1977


Thirty-seven patients with congenital bile duct cysts, including seventeen children and nine young adults, were encountered from 1960 to April 1976. Since the congenital bile duct cysts were observed in any parts of the bile duct, from the liver to the duodenum, we prefer to use the term "bile duct cyst," and we classify these cysts into six types for surgical treatment, in contrast with Alonso-Lej's classification. Based on experience with two patients in whom cancer arose from a choledochal cyst, it seems that excision of the choledochal cyst is always the most desirable operation for types Ia and Ib cysts in older children and young adults. Partial resection of intrahepatic cysts should be added in some cases of type IV-A cysts to achieve free drainage of the bile juice from the intrahepatic cysts.

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